Ophthalmologica Indonesiana
Vol 41 No 3 (2015): Ophthalmologica Indonesiana

Management of Sturge Weber Syndrome

Irawati Irfani (Department of Ophthalmology, Faculty of Medicine, Universitas Padjadjaran Cicendo National Eye Hospital, Bandung, West Java)
Sri Hardwiyani (Department of Ophthalmology, Faculty of Medicine, Universitas Padjadjaran Cicendo National Eye Hospital, Bandung, West Java)



Article Info

Publish Date
27 Apr 2016

Abstract

Background: Sturge-Weber syndrome (SWS) is a neurocutaneous syndrome, characterized by theassociation of facial port-wine hemangiomas in the trigeminal nerve distribution area, with vascularmalformation(s) of the brain (leptomeningeal angioma) with or without glaucoma. It reports a 3 monthold baby girl presented to Pediatric Ophthalmology Unit Cicendo Eye Hospital with Sturge Weber Syndrome.Case Illustration: A 3 month old baby girl presented to Pediatric Ophthalmology Unit Cicendo EyeHospital as a referral from Pediatric Department. Here in, the patient presented with port wine stain,cerebral lesion according to MRI. Her intraocular pressure on first examination was 29.33 mmHg on herright eye and 18.33 mmHg, then she was underwent examination under anesthesia and trabeculotomy-trabeculectomy procedure on December11th 2014. There was a complication of choroidal detachment aftersurgery,and the patient received oral corticosteroid to overcome the problem.On the last visit,this patient presented with controlled intraocular pressureand minimal abnormality in the retina.Conclusion:Treatment for Sturge Weber Syndrome usually symptomatic. Treatment of choice for glaucoma due to Sturge Weber Syndrome is surgical intervention rather than medical therapy.Keywords: Sturge-Weber syndrome, glaucoma

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Journal Info

Abbrev

journal

Publisher

Subject

Health Professions Medicine & Pharmacology Public Health

Description

Ophthalmologica Indonesiana is an open accessed online journal and comprehensive peer-reviewed ophthalmologist journal published by the Indonesian Ophthalmologist Association / Perhimpunan Dokter Spesialis Mata (PERDAMI). Our main mission is to encourage the important science in the clinical area of ...